Criteria for the diagnosis of Kawasaki Syndrome were proposed at an International Consensus Conference held at the University of North Carolina, Chapel Hill, North Carolina.
Lesion: vasculitis predominantly of medium-sized arteries
Vessel
Involvement
veins
possibly
venules
no
capillaries
no
arterioles
no
small arteries
yes
medium-sized arterieis
yes
large arteries
yes, including aorta
Common findings:
(1) usually occurs in children
(2) mucocutaneous lymph node syndrome
(3) involvement of the coronary arteries
Other forms of small vessel vasculitis are distinguished by:
(1) absence of mucocutaneous lymph node syndrome
(2) involvement of venules, capillaries and arterioles
(3) presence of glomerulonephritis
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