A patient with Churg-Strauss syndrome (CSS) will have a number of clinical and laboratory findings.
Findings in most patients (>= 90%):
(1) asthma
(2) eosinophilia
Common clinical and laboratory findings:
(1) constitutional symptoms (fever, fatigue, malaise, weight loss)
(2) mononeuritis multiplex
(3) cutaneous lesions
(4) rhinitis and sinusitis
(5) arthralgias and/or myalgias
(6) cardiac disease (left ventricular dysfunction, myocardial fibrosis, coronary vasculitis, pericarditis, pericardial effusion ECG abnormalities, sudden death)
(7) gastrointestinal tract involvement
(8) glomerulonephritis
(9) eosinophilic pneumonia
(10) pulmonary infiltrates on chest X-rays
(11) markedly elevated serum IgE
(12) p-ANCA in serum
Uncommon findings (<= 10%)
(1) c-ANCA in serum
(2) mediastinal lymphadenopathy
Purpose: To evaluate a patient for clinical and laboratory findings associated with Churg-Strauss Syndrome (CSS).
Specialty: Immunology/Rheumatology
Objective: criteria for diagnosis
ICD-10: M30.1,