Spontaneous rupture of the extrahepatic bile duct (SPBD) can occur in neonates and infants. It is rare and may be associated with a delay in diagnosis.

Pathogenesis: uncertain. One hypothesis is that there is a congenital weakness in the bile duct wall (often the anterior wall of the common bile duct).


The onset may be acute, subacute or chronic.


Clinical findings may include:

(1) jaundice

(2) bile peritonitis

(3) acholic stools


Cholangiography shows bile leakage from an extrahepatic bile duct.


Differential diagnosis:

(1) rupture of a choledochal cyst

(2) malformation of the extrahepatic bile ducts



(1) complete biliary obstruction secondary to scarring

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