Description

Yin et al reported a score for evaluating a neonate with Pierre Robin Sequence. The authors are from Nanjing Medical University, Southeast University and affiliated hospitals in Nanjing.


Patient selection: Pierre Robin Sequence

 

Parameters:

(1) clinical assessment

(2) body weight and growth assessment

(3) dyspnea scores

(4) Cormack-Lehane classification

 

Clinical Assessment

Finding

Points

small micromaxillary deformity or bird face with jaw retraction

absent

0

 

present

1

cleft palate or high palatine arches

absent

0

 

present

1

need of oxygenation or ventilation due to tongue posterior displacement

absent

0

 

present

1

feeding difficulties

absent

0

 

present

1

 

 

Parameter

Finding

Points

body weight and growth

weight gain > 20 g/d

0

 

weight gain 10-20 g/d

1

 

weight gain 5-10 g/d

2

 

weight gain < 5 g/d

3

 

surgical intervention required (weight loss since birth)

4

dyspnea scores

SpO2 > 95%

0

 

inspiratory dyspnea with SpO2 92-95%

1

 

inspiratory dyspnea with SpO2 88-92%, with change in position causing < 5% change in SpO2

2

 

inspiratory dyspnea with SpO2 < 88%, with change in position causing > 5% change in SpO2

3

 

continuous positive airway pressure (CPAP)

4

Cormack-Lehane

visibility of all of the glottis

0

 

visibility of most of the glottis

1

 

visibility only a glimpse of the posterior glottis joint

2

 

visibility only a glimpse of the epiglottis, without the appearance of the glottis

3

 

unable to see any anatomical portion of the throat

4

 

score =

= SUM(points for clinical assessment) + SUM(points for the other parameters)

 

Interpretation:

minimum score: 0

maximum score: 16

The higher the score the more severe the problems in the perioperative period.

A score < 10 indicates mild disease.

A score >= 10 is associated with post-extubation dyspnea and low postoperative SpO2.

A score >= 13 required laryngeal mask assisted airway management.


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