An anomalous connection between the right pulmonary vein and the inferior vena cava is termed the scimitar syndrome due to its resemblance to the Turkish sword on an AP chest X-ray.


The anomalous connection may join the inferior vena cava at its junction with the right atrium or more caudally.


Common anomalies associated with this finding:

(1) right lung hypoplasia

(2) dextroversion or dextrorotation of the heart

(3) hypoplasia of the right pulmonary artery

(4) anomalous arterial blood supply to the right lower lobe of lung from the aorta or one of its branches


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