A patient with Melkerson-Rosenthal Syndrome (MRS) may have involvement of the genitalia.
Triad of MRS:
(1) orofacial swelling (including swelling of the lower lip or cheilitis)
(2) relapsing facial paralysis
(3) fissured tongue
Genital involvement results in genital swelling.
Biopsy shows noncaseating granulomas and intralymphatic granulomas. There is hyperkeratosis, irregular acanthosis and a patchy lymphocytic infiltrate in the dermis.
Diagnosis requires exclusion of other diagnoses:
(1) Crohn's disease
(2) sarcoidosis
(3) mycobacterial or deep fungal infection
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