Rett Syndrome is an X-linked disorder that primarily affects females and which shows a range of developmental problems. It also shows a number of oral manifestations that must be managed. Because of the behavioral issues shown by patients this can be challenging.

Patient selection: Rett syndrome


Oral findings include:

(1) bruxism, with non-physiological tooth wear

(2) hypertrophy of the masseter muscles

(3) anterior open bite/malocclusion

(4) mouth breathing

(5) tongue thrusting

(6) thumb, digit or hand sucking

(7) high arched palate

(8) drooling

(9) gingivitis


In addition, the drugs used to the treat the patient may cause a range of adverse drug effects affecting the oral cavity (xerostomia, stomatitis, etc).

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