Mathieu et al developed a rating scale to describe the extent of muscular impairment in a patient with myotonic dystrophy.
Distal Muscle Weakness
Proximal Muscle Weakness
Other Signs
Grade
none
1
none or only digit flexors
myotonia, jaw and temporal wasting, ptosis, neck flexor weakness, nasal speech
2
present
with or without weakness of the elbow extensors
3
mild to moderate
4
severe
5
where:
• Severe weakness corresponds to MRC scale <= 3 (see above)
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Purpose: To evaluate muscle weakness in a patient with myotonic dystrophy using the scale of Mathieu et al.
Specialty: Surgery, orthopedic
Objective: severity, prognosis, stage
ICD-10: G71.1,