IgG4 disease may affect the male urogenital tract.
Sites involved may include:
(1) testis
(2) epididymis
(3) paratesticular tissues
(4) prostatitis
Presentation:
(1) epididymo-orchitis
(2) chronic prostatitis
(3) testicular or paratesticular mass
Histologic findings:
(1) chronic inflammation with the presence of plasma cells that mark for IgG4
(2) myofibroblastic spindle cell proliferation
(3) pseudotumor formation
Other findings:
(1) evidence of IgG4-related disease at other sites