Description

Pseudomyxoma peritonei (PMP) may be caused by lesions with histologic changes that may range from benign to malignant. Although the prognosis for a malignant tumor is worse, even benign adenomucinosis can cause significant morbidity and mortality.


 

Diagnosis

Abbreviation

Histology

disseminated peritoneal adenomucinosis

DPAM

benign (very low grade)

peritoneal mucinous carcinomatosis with intermediate (or discordant) features

PMCA-I

PMCA-I/D

intermediate

peritoneal mucinous carcinomatosis

PMCA

malignant (high grade)

 

where:

• PMCA is associated with evidence of aggressive growth including ymph node metastases and large solid tumor nodules (caking).

 

Abbreviation

Prognosis

10 Year Survival

DPAM

fair to good

68%

PMCA-I/D

guarded to poor

21%

PMCA

poor to very poor

3%

 


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