The features of a sex cord tumor with annular tubules arising in a patient with Peutz-Jeghers syndrome (PJS) are different from the tumor occurring in patients without the syndrome.
Distinguishing Feature
Patient with PJS
Patient without PJS
number
usually multiple
usually solitary
bilaterality
usually bilateral
usually unilateral
size
almost always <= 3 cm in diameter, often microscopic
usually > 3 cm in diameter
clinically malignant
very rare
some
Other findings:
(1) Calcifications are more common in tumors associated with PJS.
(2) Adenoma malignum cervix is more common in tumors associated with PJS
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