EULAR/PReS Criteria for Childhood Vasculitides: Classification

EULAR/PReS reported a classification for vasculitis in a pediatric population. This is a modification of the ACR criteria.

Patient selection: pediatric patient

Categories:

(1) predominantly large vessel vasculitis

(II) predominantly medium-sized vessel vasculitis

(IIIA) predominantly small vessel granulomatous vasculitis

(IIIB) predominantly small vessel nongranulomatous vasculitis

(IV) other vasculitis

Diagnosis	Category
Bechet's disease	other
childhood polyarteritis nodosa (PAN)	II
Churg-Strauss syndrome	IIIA
Cogan syndrome	other
cutaneous polyarteritis	II
Henoch-Schonlein purpura	IIIB
hepatitis B associated polyarteritis	other
hypocomplementic urticarial vasculitis syndrome (HUVS)	IIIB
isolated cutaneous leukocytoclastic vasculitis	IIIB
isolated vasculitis of the central nervous system (CNS)	other
Kawasaki disease	II
microscopic polyangiitis	IIIB
Takayasu arteritis	I
unclassified vasculitis	other
vasculitis associated with connective tissue disease	other
vasculitis associated with drugs	other
vasculitis associated with malignancy	other
vasculitis associated with other infections	other
Wegener's granulomatosis	IIIA

Necrotizing vasculitides:

(1) childhood polyarteritis nodosa (PAN)

(2) cutaneous polyarteritis

(3) microscopic polyangiitis

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