Description

A number of conditions can result in sclerosing cholangitis in addition to primary sclerosing cholangitis.


Conditions associated with secondary sclerosing cholangitis:

(1) Caroli’s disease

(2) Cystic fibrosis

(3) Biliary strictures (secondary to surgical trauma, chronic pancreatitis)

(4) Choledocholithiasis

(5) Eosinophilic cholangitis

 

(6) Toxic damage to bile ducts, secondary to accidental instillation of alcohol, formaldehyde, hypertonic saline into the bile ducts

 

(7) Post-traumatic sclerosing cholangitis

(8) Radiation injury

(9) Severe burns

(10) Intensive care

 

(11) Bacterial cholangitis

(12) Recurrent pyogenic cholangitis

(13) Parasitic infection (cryptosporidiosis, microsporidiosis)

(14) Cytomegalovirus infection

(15) HIV/AIDS

 

(16) Post-transplant, anastomotic strictures in liver graft

(17) Post-transplant, hepatic artery thrombosis

(18) Post-transplant, Hepatic allograft rejection (acute, chronic)

 

(19) Amyloidosis

(20) Vascular trauma

(21) Systemic vasculitis

(22) Sarcoidosis

(23) IgG4 disease

 

(24) Intra-arterial chemotherapy-related injury

(25) Transcatheter arterial embolization therapy

 

(26) Neoplasm (benign, malignant, metastatic)

(27) Hodgkin’s disease

(28) Systemic mastocytosis

(29) Hypereosinophilic syndrome


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