Pocaterra et al developed a grading scale for clinical severity of erythema nodosum leprosum (ENL). The authors are from the London School of Hygiene and Tropical Medicine, Blue Peter Research Centre Cherlapally (Hyderabad) and Universidad Cemtral de Venezuela.
Parameters:
(1) skin nodules
(2) systemic features
(3) response to steroid therapy
Skin Nodules |
Systemic Features |
Severity of ENL |
1 or 2 nontender |
nonspecific with no or low grade fever |
very mild |
few tender |
low grade fever, malaise, joint pain |
mild |
few tender |
neuritis or more than 3 systemic features |
moderate |
many tender |
high grade fever, dehydration, severe neuritis, iritis, orchitis |
severe |
Severity of ENL |
Response to Steroids |
Score |
none |
NA |
0 |
very mild |
NA |
1 |
mild |
NA |
2 |
very mild or mild |
asymptomatic |
3 |
mild to moderate |
mild symptoms |
4 |
moderate |
NA |
5 |
severe |
NA |
6 |
moderate to severe |
mild to moderate on >= 10 mg of oral prednisone |
7 (intractable) |
Specialty: Infectious Diseases, Dermatology
ICD-10: ,