Description

Cole et al reported a clinical classification for neonates with Pierre Robin sequence. The authors are from the West Midlands Regional Cleft Lip and Palate Service at Birmingham Children's Hospital in the UK.


Patient selection: Pierre Robin sequence (micrognathia, glossoptosis, cleft palate)

 

Parameters:

(1) respiratory distress when nursing

(2) glossoptosis

(3) feeding

 

Respiratory Distress

Glossoptosis

Feeding

Grade

none when nursed supine

inconsistent

satisfactory with adequate growth

1

intermittent and mild when nursed supine; none if nursed on side

consistent

some respiratory distress; failure to thrive

2

moderate to severe respiratory distress when nursed supine; respiratory distress when nursed on side

consistent

unable to feed orally

3

 

Nursing prone is discouraged for a number of reasons: obscures respiratory difficulties; problems with parental interaction, inability to detect intercostal recession.

 

A neonate who is Grade 3 usually requires:

(1) relief of airway obstruction with guaranteed airway

(2) monitoring of oxygen saturation

(3) monitoring of weight gain

(4) feeding with nasogastric tube


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