Classification of Woodard for Disease Severity in the Prune Belly Syndrome

Description

The Prune Belly Syndrome involves a congenital defect (absence, hypoplasia) of the abdominal musculature together with urogenital disease. The disease can be classified based on the severity of the findings, which correlates with survival.

Gender distribution: almost always male

Urogenital abnormalities:

(1) renal dysplasia

(2) dilation of urinary excretory system (hydronephrosis, hydroureter, hypotonic bladder)

(3) bilateral cryptorchidism

Findings	Category I	Category II	Category III
renal dysplasia	bilateral and severe	unilateral or focal	none to minimal
dilatation of the urinary tract	present	present	none to mild
urine output	scant and dilute if any	present but may be reduced	normal
pulmonary hypoplasia	present	absent	absent
oligohydramnios	present	absent	absent
other anomalies	patent urachus, complete urethral obstruction, cardiac, GI, orthopedic	abdominal distention	may be present but usually mild
survival	death during neonatal period or infancy common	usually survive infancy; may have problems with renal failure and recurrent UTIs	usually good, may have problems from recurrent UTI

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Classification of Woodard for Disease Severity in the Prune Belly Syndrome

Description

Specialty