Description

The Risk Adjustment for Congenital Heart Surgery 1 (RACHS-1) can be helpful when comparing outcomes in children undergoing surgery for congenital heart disease. The authors are from Children's Hospital Boston, Children's Hospital Philadelphia, Minnesota Children's Hospital and Beth Israel Deaconess Medical Center in Boston.


Risk Categories: from 1 to 6

 

Primary

Secondary

Risk

atrial septal defect (ASD)

ASD secundum, sinus venosus ASD, patent foramen ovale

1

aortopexy

 

1

patent ductus arteriosus

age > 30 days

1

coarctation of the aorta

age > 30 days

1

anomalous pulmonary venous connection, partial

 

1

aortic valvotomy or valvuloplasty

age > 30 days

2

subaortic stenosis

 

2

pulmonary valvotomy or valvuloplasty

 

2

pulmonary valve replacement

 

2

right ventricular infundibulectomy

 

2

pulmonary outflow tract augmentation

 

2

coronary artery fistula

 

2

atrial AND ventricular septal defects

 

2

atrial septal defect (ASD)

primum

2

ventricular septal defect (VSD)

 

2

ventricular septal defect AND pulmonary valvotomy

 

2

ventricular septal defect AND infundibular resection

 

2

ventricular septal defect closure AND pulmonary artery band removal

 

2

septal defect, unspecified

 

2

tetralogy of Fallot, total

 

2

anomalous pulmonary veins, total

age > 30 days

2

Glenn shunt

 

2

vascular ring surgery

 

2

aorto-pulmonary window

 

2

coarctation of the aorta

age <= 30 days

2

pulmonary artery stenosis

 

2

pulmonary artery transection

 

2

common atrium

 

2

left ventricular to right atrial shunt

 

2

aortic valve replacement

 

3

Ross procedure

 

3

left ventricular outflow tract

patch

3

ventriculomyotomy

 

3

aortoplasty

 

3

mitral valvotomy or valvuloplasty

 

3

mitral valve replacement

 

3

tricuspid valve valvectomy

 

3

tricuspid valvotomy or valvuloplasty

 

3

tricuspid valve replacement

 

3

tricuspid valve repositioning in Ebstein anomaly

age > 30 days

3

anomalous coronary artery without intrapulmonary tunnel

 

3

anomalous coronary artery with intrapulmonary tunnel (Takeuchi)

 

3

aortic valve, semilunar

 

3

pulmonary valve, semilunar

 

3

right ventricular to pulmonary artery conduit

 

3

left ventricular to pulmonary artery conduit

 

3

double-outlet right ventricle with or without repair of right ventricular obstruction

 

3

Fontan procedure

 

3

atrioventricular canal, transitional or complete

with or without valve replacement

3

pulmonary artery banding

 

3

tetralogy of Fallot with pulmonary atresia

 

3

cor triatriatum

 

3

shunt, systemic to pulmonary artery

 

3

atrial switch operation

 

3

arterial switch operation

 

3

anomalous pulmonary artery

reimplantation

3

annuloplasty

 

3

coarctation AND ventricular septal defect

 

3

intracardiac tumor resection

 

3

aortic valvotomy or valvuloplasty

age <= 30 days

4

Konno procedure

 

4

repair of complex anomaly (single ventricle) by ventricular septal defect enlargement

 

4

anomalous pulmonary veins, total

age <= 30 days

4

atrial septectomy

 

4

transposition, ventricular septal defect AND subpulmonary stenosis (Rastelli)

 

4

atrial switch operation with ventricular septal defect closure

 

4

atrial switch operation with repair of subpulmonary stenosis

 

4

arterial switch operation with pulmonary artery band removal

 

4

arterial switch operation with ventricular septal defect closure

 

4

arterial switch operation with repair of subpulmonary stenosis

 

4

truncus arteriosus

 

4

aortic arch, hypoplastic or interrupted, without ventricular septal defect closure

 

4

aortic arch, hypoplastic or interrupted, with ventricular septal defect closure

 

4

transverse arch graft

 

4

tetralogy of Fallot and pulmonary atresia

unifocalization

4

double switch

 

4

tricuspid valve repositioning for neonatal Ebstein anomaly

age <= 30 days

5

truncus arteriosus AND interrupted arch

 

5

left heart syndrome, hypoplastic

Stage 1 repair (Norwood procedure)

6

left heart syndrome, nonhypoplastic

Stage 1 repair

6

Damus-Kaye-Stansel procedure

 

6

 

Resorted

 

Primary

Secondary

Risk

annuloplasty

 

3

anomalous coronary artery with intrapulmonary tunnel (Takeuchi)

 

3

anomalous coronary artery without intrapulmonary tunnel

 

3

anomalous pulmonary artery

reimplantation

3

anomalous pulmonary veins, total

age > 30 days

2

anomalous pulmonary veins, total

age <= 30 days

4

anomalous pulmonary venous connection, partial

 

1

aortic arch, hypoplastic or interrupted, with ventricular septal defect closure

 

4

aortic arch, hypoplastic or interrupted, without ventricular septal defect closure

 

4

aortic valve replacement

 

3

aortic valve, semilunar

 

3

aortic valvotomy or valvuloplasty

age > 30 days

2

aortic valvotomy or valvuloplasty

age <= 30 days

4

aortopexy

 

1

aortoplasty

 

3

aorto-pulmonary window

 

2

arterial switch operation

 

3

arterial switch operation with pulmonary artery band removal

 

4

arterial switch operation with repair of subpulmonary stenosis

 

4

arterial switch operation with ventricular septal defect closure

 

4

atrial AND ventricular septal defects

 

2

atrial septal defect (ASD)

ASD secundum, sinus venosus ASD, patent foramen ovale

1

atrial septal defect (ASD)

primum

2

atrial septectomy

 

4

atrial switch operation

 

3

atrial switch operation with repair of subpulmonary stenosis

 

4

atrial switch operation with ventricular septal defect closure

 

4

atrioventricular canal, transitional or complete

with or without valve replacement

3

coarctation AND ventricular septal defect

 

3

coarctation of the aorta

age > 30 days

1

coarctation of the aorta

age <= 30 days

2

common atrium

 

2

repair of complex anomaly (single ventricle) by ventricular septal defect enlargement

 

4

cor triatriatum

 

3

coronary artery fistula

 

2

Damus-Kaye-Stansel procedure

 

6

double switch

 

4

double-outlet right ventricle with or without repair of right ventricular obstruction

 

3

Fontan procedure

 

3

Glenn shunt

 

2

intracardiac tumor resection

 

3

Konno procedure

 

4

left heart syndrome, hypoplastic

Stage 1 repair (Norwood procedure)

6

left heart syndrome, nonhypoplastic

Stage 1 repair

6

left ventricular outflow tract

patch

3

left ventricular to pulmonary artery conduit

 

3

left ventricular to right atrial shunt

 

2

mitral valve replacement

 

3

mitral valvotomy or valvuloplasty

 

3

patent ductus arteriosus

age > 30 days

1

pulmonary artery banding

 

3

pulmonary artery stenosis

 

2

pulmonary artery transection

 

2

pulmonary outflow tract augmentation

 

2

pulmonary valve replacement

 

2

pulmonary valve, semilunar

 

3

pulmonary valvotomy or valvuloplasty

 

2

right ventricular infundibulectomy

 

2

right ventricular to pulmonary artery conduit

 

3

Ross procedure

 

3

septal defect, unspecified

 

2

shunt, systemic to pulmonary artery

 

3

subaortic stenosis

 

2

tetralogy of Fallot and pulmonary atresia

unifocalization

4

tetralogy of Fallot with pulmonary atresia

 

3

tetralogy of Fallot, total

 

2

transposition, ventricular septal defect AND subpulmonary stenosis (Rastelli)

 

4

transverse arch graft

 

4

tricuspid valve replacement

 

3

tricuspid valve repositioning for neonatal Ebstein anomaly

age <= 30 days

5

tricuspid valve repositioning in Ebstein anomaly

age > 30 days

3

tricuspid valve valvectomy

 

3

tricuspid valvotomy or valvuloplasty

 

3

truncus arteriosus

 

4

truncus arteriosus AND interrupted arch

 

5

vascular ring surgery

 

2

ventricular septal defect (VSD)

 

2

ventricular septal defect AND infundibular resection

 

2

ventricular septal defect AND pulmonary valvotomy

 

2

ventricular septal defect closure AND pulmonary artery band removal

 

2

ventriculomyotomy

 

3

 


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