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Description

The different types of autoimmune myositis may be associated with different autoantibodies.


Polymyositis

 

Autoantibody

Target

Also Found In

anti-ARS (anti-Jo1, anti-Ha, others)

tRNA synthetase

antisynthetase syndrome

 

Dermatomyositis

 

Autoantibody

Target

Also Found In

anti-Mi-2

NuRD subunit

 

anti-TIFI-gamma

transcriptional intermediary factor 1gamma

paraneoplastic DM

anti-NXP-2

nuclear matrix protein 2

paraneoplastic DM

anti-MDA5

melanoma dedifferentiation associated protein 5

ILD

anti-SAE

SUMO-1 activating enzyme

 

 

Necrotizing Myopathy

 

Autoantibody

Target

Also Found In

anti-SRP

signal recognition particle

 

anti-HMGCR

3-hydroxy-3-methyl-glutaryl-CoA reductase

statin use

 

Overlap with Polymyositis/Dermatomyositis

 

Autoantibody

Target

Also Found In

anti-Ro/SSA

Ro52 subunit

SLE, Sjogren's

anti-PM/Scl

 

scleroderma

anti-Ku

 

SLE, Sjogren's, ILD

anti-U1RNP

 

LE, MCTD

 


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