Congenital mitral valve disease (CMVD) can be classified based on the anatomic distribution of the structural defects.
Requirements:
(1) abnormality involving the mitral valve
(2) functional left ventricle
Location of Abnormality
|
Term
|
Type
|
above the level of the annulus or valve leaflets
|
supravalvular
|
1
|
involving the annulus and/or valve leaflets
|
valvular
|
2
|
involving the chordae tendineae and/or papillary muscles
|
subvalvular
|
3
|
combination of 2 or 3 of the above types
|
mixed
|
4
|