Relapsing polychondritis may be encountered in patients with a number of systemic disorders. Management of the polychrondritis may be influenced by management of the associated systemic disorder.
Disorders associated with relapsing polychondritis:
(1) Behcet’s disease
(2) Wegener’s granulomatosis
(3) polyarteritis nodosa (PAN)
(4) Takayasu arteritis
(5) leukocytoclastic vasculitis
(6) Cogan syndrome
(7) Henoch-Schonlein purpura
(8) thromboangiitis obliterans
(9) rheumatoid arthritis (RA)
(10) systemic lupus erythematosus (SLE)
(11) Sjogren syndrome
(12) juvenile chronic arthritis
(13) myelodysplastic syndrome
(14) hematologic malignancy
(15) cryoglobulinemia
(16) pernicious anemia
(17) thymoma
(18) autoimmune endocrinopathy
(19) vitiligo
(20) myasthenia gravis
(21) primary biliary cirrhosis (PBC)
(22) dermatitis herpetiformis (DH)
(23) atopic dermatitis
(24) lichen planus
(25) psoriasis
(26) inflammatory bowel disease
(27) diabetes mellitus
(28) Familial Mediterranean Fever (FMF)
(29) panniculitis
(30) retroperitoneal fibrosis
(31) Sweet syndrome
(32) spondyloarthropathy
Many of these conditions involve one or more of the following:
(1) vasculitis
(2) autoimmunity
(3) cryoglobulinemia
Purpose: To evaluate a patient with relapsing polychondritis for systemic disorders that may be associated with it.
Specialty: Immunology/Rheumatology
Objective: laboratory tests, complications, comorbid conditions, prevention
ICD-10: M94.1,