Description

Idiopathic retinal vasculitis, aneurysms, and neuro-retinitis (IRVAN) is a rare condition of unknown cause.


 

Clinical findings:

(1) bilateral decreased visual acuity

(2) often a poor response to oral steroids

(3) often reversible with time unless serious complications occur

 

Ocular findings are bilateral:

(1) posterior retinal vasculitis

(2) retinitis

 

Features of vasculitis:

(1) vascular occlusion with decreased perfusion, often with ischemia

(2) macroaneurysms of the retinal arteries

 

Features of retinitis:

(1) edema (optic disc, other)

(2) exudative maculopathy

 

Diagnosis requires exclusion of other causes of vasculitis and neuroretinitis.

 

Complications:

(1) vitreous hemorrhage

(2) traction-type retinal detachment

 


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