Morgen and Superina reported a classification system for congenital extrahepatic portosystemic shunt (Abernathy malformation, CEPSh).
The Abernathy malformation is a congenital diversion of portal blood away from the liver. This may be due to either:
(1) side-to-side shunt
(2) end-to-side shunt.
It may be associated with additional congenital malformations.
Parameters:
(1) status of intrahepatic portal veins
(2) drainage of superior mesenteric and splenic veins into the inferior vena cava (IVC)
Intrahepatic Portal Vein
Drainage of SMV and SV into IVC
Type
absent
drain separately into IVC
Ia
merge into common trunk that drains into IVC
Ib
some patent
important collaterals result in shunting
II
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Specialty: Cardiology, Genetics, Pedatrics
ICD-10: ,