EULAR developed a disease activity index for primary Sjogren's syndrome called the ESSDAI. This consists of 12 subscores measuring various components of disease activity. The authors are from the European League Against Rheumatism Sjogren's Task Force.
Patient selection: primary Sjogren's syndrome
Exclude: pulmonary changes due to another disorder such as smoking.
Parameters for pulmonary subscore:
(1) cough or bronchial involvement
(2) high resolution CT (HRCT) evidence of interstitial lung disease
|
Parameter |
Finding |
Points |
|
cough or bronchial involvement |
none |
0 |
|
|
without radiographic abnormalities |
1 |
|
|
with radiographic abnormalities |
2 |
|
interstitial lung disease on HRCT |
none |
0 |
|
|
present with normal pulmonary function tests, no dyspnea |
1 |
|
|
present with moderate pulmonary disease (NYHA II) and dyspnea on exercise |
2 |
|
|
present with severe pulmonary disease (NYHA III or IV) and dyspnea at rest |
3 |
|
Lung Disease |
Findings |
|
mild |
FVC >= 80% predicted, DLco >= 70% |
|
moderate |
FVC < 80% and >= 40%, DLco < 70% and >= 40% |
|
severe |
FVC < 60% predicted, DLco < 40% |
subscore weighting: 5
subscore for pulmonary findings =
= MAX(points for the parameters) * (weighting)
Interpretation:
• minimum subscore: 0
• maximum subscore: 15
|
Subscore |
Disease Activity |
|
0 |
no |
|
5 |
low |
|
10 |
moderate |
|
15 |
high |
Specialty: Immunology/Rheumatology
