Schnitzler's Syndrome is a rare form of urticarial vasculitis.
Key findings:
(1) urticarial skin lesions
(2) monoclonal IgM gammopathy
(3) leukocytoclastic vasculitis on skin biopsy
Associated clinical findings:
(1) lymphadenopathy
(2) intermittent fevers
(3) sensorimotor neuropathy
(4) renal failure
(5) hepatosplenomegaly
(6) osteosclerotic bone lesions with bone pain
(7) arthralgias
(8) myalgias
Associated laboratory findings:
(1) elevated erythrocyte sedimentation rate (ESR)
(2) leukocytosis
(3) reduced complement concentrations
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Specialty: Immunology/Rheumatology
ICD-10: ,