Description

A patient with Churg-Strauss syndrome (CSS) will have a number of clinical and laboratory findings.


 

Findings in most patients (>= 90%):

(1) asthma

(2) eosinophilia

 

Common clinical and laboratory findings:

(1) constitutional symptoms (fever, fatigue, malaise, weight loss)

(2) mononeuritis multiplex

(3) cutaneous lesions

(4) rhinitis and sinusitis

(5) arthralgias and/or myalgias

(6) cardiac disease (left ventricular dysfunction, myocardial fibrosis, coronary vasculitis, pericarditis, pericardial effusion ECG abnormalities, sudden death)

(7) gastrointestinal tract involvement

(8) glomerulonephritis

(9) eosinophilic pneumonia

(10) pulmonary infiltrates on chest X-rays

(11) markedly elevated serum IgE

(12) p-ANCA in serum

 

Uncommon findings (<= 10%)

(1) c-ANCA in serum

(2) mediastinal lymphadenopathy

 


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