A woman with an ovarian tumor may develop an autoimmune hemolytic anemia.
Clinical features:
(1) onset of a hemolytic anemia with a positive direct antiglobulin test
(2) presence of an ovarian tumor
(3) poor response to corticosteroid therapy and/or splenectomy
(4) disappearance of the hemolytic anemia following resection of the ovarian tumor
The ovarian tumor is classically a mature teratoma (dermoid cyst) but the syndrome may occur with other types of ovarian tumors.
To read more or access our algorithms and calculators, please log in or register.
Specialty: Immunology/Rheumatology
