Description

The disability experienced by a patient with adrenoleukodystrophy can be assessed using the adrenoleukodystrophy disability rating scale (ALD-DRS).


 

Parameters:

(1) learning and cognitive ability

(2) sensory problems

(3) neurological (including coordination)

(4) assistance required

 

The first 3 items are graded as:

(1) none

(2) mild

(3) moderate

(4) severe

 

Maximal Grade

Assistance Required

Disability Level

none

none

0

mild

none

I

moderate

few areas

II

severe

most areas

III

loss of cognitive ability with disorientation

constant in all areas

IV

 


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